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image/svg+xml Jakob Voss, based on art designer at PLoS, modified by Wikipedia users Nina and Beao Closed Access logo, derived from PLoS Open Access logo. This version with transparent background. http://commons.wikimedia.org/wiki/File:Closed_Access_logo_transparent.svg Jakob Voss, based on art designer at PLoS, modified by Wikipedia users Nina and Beao
Nature
Article . 1997 . Peer-reviewed
License: Springer TDM
Data sources: Crossref
Nature
Article . 1997
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Scrambler and yotari disrupt the disabled gene and produce a reeler -like phenotype in mice

Authors: M, Sheldon; D S, Rice; G, D'Arcangelo; H, Yoneshima; K, Nakajima; K, Mikoshiba; B W, Howell; +3 Authors

Scrambler and yotari disrupt the disabled gene and produce a reeler -like phenotype in mice

Abstract

Formation of the mammalian brain requires choreographed migration of neurons to generate highly ordered laminar structures such as those in the cortices of the forebrain and the cerebellum. These processes are severely disrupted by mutations in reelin which cause widespread misplacement of neurons and associated ataxia in reeler mice. Reelin is a large extracellular protein secreted by pioneer neurons that coordinates cell positioning during neurodevelopment. Two new autosomal recessive mouse mutations, scramble and yotari have been described that exhibit a phenotype identical to reeler. Here we report that scrambler and yotari arise from mutations in mdab1, a mouse gene related to the Drosophila gene disabled (dab). Both scrambler and yotari mice express mutated forms of mdab1 messenger RNA and little or no mDab1 protein. mDab1 is a phosphoprotein that appears to function as an intracellular adaptor in protein kinase pathways. Expression analysis indicates that mdab1 is expressed in neuronal populations exposed to Reelin. The similar phenotypes of reeler, scrambler, yotari and mdab1 null mice indicate that Reelin and mDab1 function as signalling molecules that regulate cell positioning in the developing brain.

Keywords

Extracellular Matrix Proteins, Mice, Inbred C3H, Cell Adhesion Molecules, Neuronal, Serine Endopeptidases, Brain, Chromosome Mapping, Gene Expression, Nerve Tissue Proteins, Axons, Mice, Inbred C57BL, Mice, Mice, Neurologic Mutants, Reelin Protein, Phenotype, Mutation, Animals, RNA, Messenger, Crosses, Genetic, In Situ Hybridization

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Powered by OpenAIRE graph
citations
This is an alternative to the "Influence" indicator, which also reflects the overall/total impact of an article in the research community at large, based on the underlying citation network (diachronically).
BIP!Citations provided by BIP!
popularity
This indicator reflects the "current" impact/attention (the "hype") of an article in the research community at large, based on the underlying citation network.
BIP!Popularity provided by BIP!
influence
This indicator reflects the overall/total impact of an article in the research community at large, based on the underlying citation network (diachronically).
BIP!Influence provided by BIP!
impulse
This indicator reflects the initial momentum of an article directly after its publication, based on the underlying citation network.
BIP!Impulse provided by BIP!
597
Top 1%
Top 1%
Top 0.1%